The determinants of survival among adults with cystic fibrosis—a cohort study

Table 3 Number and percentage of adult CF people in the category of CFTR mutation, nutritional status, lung function, and Pseudomonas aeruginosa infection

Variable	Number	N (%)
Genotype
I–III/I–III	40	32.26
I–III/IV–V or I–III/u	31	25.00
IV–V/IV–V	24	19.35
u/u	29	23.39
FEV₁%
FEV₁% > 70	31	25.00
FEV₁% 70–40	47	37.90
FEV₁% < 40	46	37.10
Pseudomonas aeruginosa
Pseudomonas culture-negative	36	29.03
Non-MDR	37	29.84
MDR	24	19.36
XDR/PDR	27	21.77
Nutritional status
BMI ≥ 25	5	4.03
BMI 18.5–24.9	74	59.68
BMI 17–18.49 (class II malnutrition)	24	19.35
BMI 16–16.99 (class I malnutrition)	9	7.26
BMI < 16 (emaciation)	12	9.68

I–III/I–III patients with severe types of mutation on both alleles, I–III/IV–V or I–III/u patients with a severe type of mutation on one allele and mild or unclassified mutation on another allele, IV–V/IV–V patients with mild types of mutation on both alleles, u/u patients with unclassified mutations on both alleles, BMI body mass index, FEV₁% forced expiratory volume in one second, Non-MDR non-multidrug-resistant patients, MDR multidrug-resistant patients, PDR+XDR pandrug-resistant and extensively drug-resistant patients

ISSN: 1880-6805